Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension

Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension

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Superficial siderosis (SS) of the nervous system is a 3m speedglas 9002nc rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration.The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs.Here we describe an pantaloni bianchi neonato atypical case of infratentorial SS evolving with acute intracranial hypertension in the absence of typical chronic signs.